Scientific Program
 
Scientific ProgramSearch Abstract
 
Session
 
Red blood cells and Iron I
Date: Friday, 05 June 2009
Time:17:45-19:00
Room:
 
17:45-19:00
EFFICACY AND SAFETY OF DEFERASIROX IN REDUCING MYOCARDIAL SIDEROSIS IN PATIENTS WITH ?-THALASSAEMIA MAJOR 0193
Pennell, Dudley, Porter, John B., Cappellini, Maria Domenica, Chan, Lee Lee, El-Beshlawy, Amal, Aydinok, Yesim, Ibrahim, Hishamshah, Li, Chi-Kong, Viprakasit, Vip, Elalfy, Mohsen, Kattamis, Antonis, Smith, Gillian, Habr, Dany, Domokos, Gabor, Hmissi, Abdel, Taher, Ali (London, United Kingdom)
 
17:45-19:00
LABILE PLASMA IRON LEVELS IN HEAVILY IRON-OVERLOADED PATIENTS WITH TRANSFUSION-DEPENDENT ANAEMIAS IN RESPONSE TO DEFERASIROX THERAPY: RESULTS FROM THE LARGE-SCALE, PROSPECTIVE 1-YEAR EPIC TRIAL 0194
Kattamis, Antonis, El-Beshlawy, Amal, Seymour, John F., Li, Chi-Kong, Nick, Hanspeter, Habr, Dany, Domokos, Gabor, Roubert, Bernard, Cappellini, Maria Domenica (Athens, Greece)
 
17:45-19:00
THE EFFICACY OF IRON CHELATOR REGIMES IN REDUCING CARDIAC AND HEPATIC IRON IN PATIENTS WITH THALASSAEMIA MAJOR: A CLINICAL OBSERVATIONAL STUDY 0195
Berdoukas, Vasilios, Chouliaras, Giorgos , Moraitis, Panagiotis, Zannikos, Kirykos , Berdoussi, Eleni, Ladis, Vassilis (ATHENS, Greece)
 
17:45-19:00
INCREASED PLASMA LEVELS OF NGAL AND IL-18 CORRELATE WITH REDUCED GFR PROVIDING EVIDENCE OF TUBULOGLOMERULAR DEFECT IN PATIENTS WITH HBS/BETA-THALASSEMIA 0196
Papassotiriou, Ioannis, Margeli, Alexandra , Hantzi, Eugenia , Terpos, Evangelos, Voskaridou, Ersi (Athens, Greece)
 
17:45-19:00
ANALYSIS OF IRON HOMEOSTASIS AND ERYTHROID ACTIVITY IN A COHORT OF LOW-RISK MYELODYSPLASTIC PATIENTS 0197
Messa, Emanuela, Maffè, Chiara, Volpe, Gisella, Campostrini, Natascia, Gioia, Daniela, Levis, Alessandro, Cilloni, Daniela, Girelli, Domenico, Camaschella, Clara, Saglio, Giuseppe (Orbassano, Italy)
 
17:45-19:00
MYOCARDIAL LESIONS AND IRON DEPOSITS AFTER TREATMENT WITH ANTHRACYCLINES 0198
CASCALES, ALMUDENA, PASTOR, F., SANCHEZ-VEGA, B., CORRAL, J, VICENTE, V., AYALA, F. (MURCIA, Spain)
 
17:45-19:00
ASSESSMENT OF SAFETY IN PATIENTS RECEIVING LONGER-TERM IRON CHELATION THERAPY WITH DEFERASIROX WHO HAD ACHIEVED SERUM FERRITIN LEVELS OF <1000 NG/ML DURING THE STUDY COURSE 0199
Porter, John, Piga, Antonio, Cohen, Alan, Ford, John M., Bodner, Janet, Cappellini, Maria Domenica (London, United Kingdom)
 
17:45-19:00
SAFETY AND EFFICACY OF IRON CHELATION THERAPY WITH DEFERASIROX IN PATIENTS WITH SICKLE CELL DISEASE (SCD): 3.5-YEAR FOLLOW-UP 0200
Vichinsky, Elliott, Coates, Thomas, Thompson, Alexis, Bernaudin, Françoise, Lagrone, Darlene, Dong, Victor, Heeney, Matthew (Oakland, CA, United States of America)
 
17:45-19:00
DEFERASIROX IN PAEDIATRIC PATIENTS WITH THALASSAEMIA MAJOR: 1-YEAR RESULTS FROM A LARGE PAEDIATRIC COHORT ENROLLED IN THE PROSPECTIVE, MULTICENTRE EPIC STUDY 0201
Filosa, Aldo, Elalfy, Mohsen, Li, Chunfu, Lai, Yongrong, Chan, Lee Lee, Sutcharitchan, Pranee, Habr, Dany, Domokos, Gabor, Roubert, Bernard, El-Beshlawy, Amal (Naples, Italy)
 
17:45-19:00
DELETION IN THE LDLR1 & 2 DOMAINS IN THE TMPRSS6 GENE IN A CHILD CAUSES IRIDA WITH EXTREMELY HIGH HEPCIDIN LEVEL 0202
Tchou, Isabelle, Diepold , Miriam MD, Neerman-Arbez, Marguerite MD, Beris, Photis MD (P) (Geneva, Switzerland)
 
17:45-19:00
OUTCOMES OF PATIENTS WITH SICKLE CELL DISEASE ADMITTED TO THE INTENSIVE THERAPY UNIT – A SINGLE INSTITUTION EXPERIENCE 0203
Gardner, Kate, Bell, Cathy, Allman, Marlene, Ervine, Max, Thein, Swee Lay, Awogbade, Moji (London, United Kingdom)
 
17:45-19:00
TREATMENT WITH DEFERASIROX EFFECTIVELY DECREASES IRON BURDEN IN PATIENTS WITH THALASSEMIA INTERMEDIA 0204
Voskaridou, Ersi, Konstantinidou, M., Douskou, M., Plata, E., Papadakis, M., Delaki, E.E., Christoulas, D., Terpos, E. (Athens, Greece)
 
17:45-19:00
ACUTE SPLENIC SEQUESTRATION IN SICKLE CELL DISEASE (SCD) 0205
Brousse, Valentine, Lesprit, E., Bernaudin, F., Odievre, M.H., Guitton, C., Quinet, B., Dangiolo, S., De Montalembert, M. (Paris, France)
 
17:45-19:00
IRON CHELATION THERAPY WITH DEFERASIROX FOR TRANSFUSIONAL IRON-OVERLOADED PATIENTS WITH APLASTIC ANAEMIA AND OTHER RARE ANAEMIAS 0206
Porter, John, Yoon, Sung-Soo, Shen, Zhi Xiang, Thein, Swee Lay, Lin, Kai-Hsin, Habr, Dany, Domokos, Gabor, Roubert, Bernard, Lee, Jong Wook (London, United Kingdom)
 
17:45-19:00
A CLOSER LOOK AT CELLULAR IRON METABOLISM IN IRP2 DEFICIENT ERYTHROBLASTS 0207
Schranzhofer, Matthias, Galy, Bruno, Schifrer, Manfred, Hentze, Matthias, Muellner, Ernst, Ponka, Prem (Montreal, Canada)
 
17:45-19:00
ASSESSMENT OF NON-TRANSFERRIN BOUND IRON IN THALASSEMIC SERA USING A NEW FLUORESCENCE BASED ASSAY 0208
Gohil, Nivedita K, Sharma, Manisha, Saxena, Renu (P) (New Delhi, India)
 
17:45-19:00
DEFERASIROX SIGNIFICANTLY REDUCES IRON BURDEN IN HEAVILY IRON-OVERLOADED PATIENTS WITH BETA-THALASSAEMIA: 2.7 YEAR RESULTS FROM THE ESCALATOR STUDY 0209
Taher, Ali, El-Beshlawy, Amal, Elalfy, Mohsen, Al Zir, Kusai, Daar, Shahina, Habr, Dany, Kriemler-Krahn, Ulrike, Roubert, Bernard, Al Jefri, Abdullah (Beirut, Lebanon)